Introduction: Apert syndrome is a challenging syndromic condition for health care specialists because it affects the patient's overall physical, oral and behavioral health. Knowledge of the protocols to be followed and dental management by the operator of patients with AS are of great importance in the dental field, allowing for adequate and guided craniofacial and behavioral control of the patient. Objective: The objective of this article is to present a clinical case that shows an adequate treatment plan for a patient with Apert syndrome. Methodology: an objective description of the clinical case is made with analysis of a total of articles, including review and original articles, as well as clinical cases, of which 12 bibliographies were used because the other articles were not relevant for this study. The sources of information were indexed journals, as well as search engines such as PubMed, Google Scholar and Cochrane; the terms used for the information search were: Apert syndrome, acrocephalosyndactyly, craniosynostosis, dental care. Results: We report a 15-year-old female patient who presented the characteristic triad of Apert syndrome: craniosynostosis, facial malformations and symmetrical syndactyly. Conclusions: Knowledge of the disease by health professionals will be of vital importance in order to develop appropriate strategies and efficient care protocols for patients with Apert syndrome, resulting in a better quality of life for the patient in the short and long term.